CSC Congenital Heart Disease Surgery 2

Question 1

The bidirectional Glenn procedure connects which two structures?

Accepted Answer

Superior vena cava end-to-side to the right pulmonary artery

Answer

Inferior vena cava end-to-side to the main pulmonary artery

Answer

Subclavian artery side-to-side to the pulmonary artery

Answer

Right atrium to the right pulmonary artery via a tunnel

Question 2

At what approximate age is Fontan completion typically performed following the bidirectional Glenn procedure?

Accepted Answer

2 to 4 years of age

Answer

1 to 3 months of age

Answer

6 to 12 months of age

Answer

8 to 12 years of age

Question 3

Coarctation of the aorta most commonly occurs at which anatomical location?

Accepted Answer

Juxtaductal position near the insertion of the ligamentum arteriosum

Answer

Ascending aorta proximal to the innominate artery origin

Answer

Aortic arch between the left common carotid and left subclavian arteries

Answer

Descending thoracic aorta at the level of the diaphragm

Question 4

Total anomalous pulmonary venous connection (TAPVC) requires urgent surgical repair when which condition is present?

Accepted Answer

Pulmonary venous obstruction causing severe cyanosis and pulmonary edema

Answer

Mild right ventricular dilation on echocardiogram

Answer

Bidirectional shunting at the atrial level

Answer

Pulmonary artery pressure equal to 50% of systemic pressure

Question 5

In Ebstein anomaly, what is the primary anatomical abnormality of the tricuspid valve?

Accepted Answer

Apical displacement of the septal and posterior leaflets into the right ventricle

Answer

Prolapse of the anterior leaflet into the right atrium during systole

Answer

Fusion of all three leaflets causing severe tricuspid stenosis

Answer

Absence of the septal leaflet with a single large anterior leaflet

Question 6

Which surgical technique for Ebstein anomaly repair involves detaching and rotating the available leaflet tissue to create a cone-shaped valve?

Accepted Answer

Cone reconstruction (da Silva technique)

Answer

Konno-Rastan aortoventriculoplasty

Answer

Damus-Kaye-Stansel anastomosis

Answer

Danielson repair with posterior plication

Question 7

In the Collett and Edwards classification, what defines Type I truncus arteriosus?

Accepted Answer

A short main pulmonary artery segment arising from the left side of the common truncal root

Answer

Separate pulmonary arteries arising from the posterior truncus with no main pulmonary artery segment

Answer

Pulmonary arteries arising as collaterals from the descending aorta

Answer

Complete atresia of the pulmonary valve with ductal-dependent pulmonary flow